PO-02-232 CARDIONEURAL ABLATION IN THE MANAGEMENT OF LONG QT SYNDROME, TYPE 7
نویسندگان
چکیده
Vasovagal syncope is a complex interaction of neurologic and cardiovascular mechanisms resulting in cardiac inhibition by the parasympathetic nervous system via vagus nerve associated ganglionic plexi. Some types tachycardia may be induced bradycardia, LQT type 3 being most common example. In these patients, pacemaker sometimes indicated to avoid bradycardia trigger for tachycardia. Cardioneural ablation (CNA) an emerging therapy that offers potential abolishing vagal-induced bradycardia. It commonly used treat vasovagal but it also provide benefit patients with bradycardia-induced tachyarrhythmias. We present case patient Long QT 7 who had asystolic pause which run nonsustained VT. was utilized intention avoiding future triggering An 8-year-old female past-medical history Andersen-Tawil Syndrome (Long 7). She two syncopal events suggested vagal etiology. After loop monitor placement, she third event, recorded period sinus culminating 6.3 second pause, followed 6 beat VT, cycle length 200-260 msec. considered as means bradycardic events. Procedure performed under general anesthesia. Electroanatomic mapping (Ensite Precision) create 3D geometry. The same system, coupled transthoracic ultrasound, guide transseptal puncture. Sinus could at baseline stimulation. Areas fractionated signals were mapped high atrial septum between right upper pulmonary vein fossa ovalis; roof coronary sinus. Patient known have persistent left SVC These areas targeted ablation. Post ablation, no inducible tolerated procedure well, without complication. CNA shows promise treatment syncope. However, there other clinical settings finds utility. Conditions might include syndrome, 3, Brugada possibly Congenital Central Hypoventilation syndrome. Further investigation needed elucidate safety efficacy settings.
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ژورنال
عنوان ژورنال: Heart Rhythm
سال: 2023
ISSN: ['1556-3871', '1547-5271']
DOI: https://doi.org/10.1016/j.hrthm.2023.03.1602